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Dystrophin isoform Dp116 (peripheral nerve)

(last modified March 2, 1999)


Submitted to GenBank


LOCUS       Dp116        5623 bp    mRNA            PRI       20-JAN-1998
DEFINITION  Human dystrophin cDNA isoform Dp116 (peripheral nerve).
ACCESSION   Dp116
KEYWORDS    .
SOURCE      human.
  ORGANISM  Homo sapiens
            Eukaryota; Metazoa; Chordata; Vertebrata; Mammalia; Eutheria;
            Primates; Catarrhini; Hominidae; Homo.
REFERENCE   1  (bases 1 to 106)
  AUTHORS   Byers,T.J., Lidov,H.G. and Kunkel,L.M.
  TITLE     An alternative dystrophin transcript specific to peripheral nerve
  JOURNAL   Nature Genet. 4 (1), 77-81 (1993)
  MEDLINE   93291881
REFERENCE   2  (bases 1 to 5623)
  AUTHORS   den Dunnen,J.T.
  TITLE     Transcripts of the human dystrophin gene
  JOURNAL   Unpublished
  REMARK    More details regarding the nomenclature used, the annotations (e.g.
            proper references), RFLP's and mutations found in DMD, BMD and
            XLDCM patients, can be obtained from http://www.dmd.nl/
 
COMMENT     Constructed consensus sequence of GenBank S62617 and M18533.
FEATURES             Location/Qualifiers
     source          1..5623
                     /organism="Homo sapiens"
                     /db_xref="taxon:9606"
                     /chromosome="X"
                     /map="Xp21.2"
     5'UTR           <1..61
     CDS             62..2932
                     /note="alternative splicing at the 3'end gives several
                     Dp116 isoforms."
                     /codon_start=1
                     /product="dystrophin Dp116"
                     /translation="MLHRKTYHVKDLQGEIEAHTDVYHNLDENSQKILRSLEGSDDAV
                     LLQRRLDNMNFKWSELRKKSLNIRSHLEASSDQWKRLHLSLQELLVWLQLKDDELSRQ
                     APIGGDFPAVQKQNDVHRAFKRELKTKEPVIMSTLETVRIFLTEQPLEGLEKLYQEPR
                     ELPPEERAQNVTRLLRKQAEEVNTEWEKLNLHSADWQRKIDETLERLQELQEATDELD
                     LKLRQAEVIKGSWQPVGDLLIDSLQDHLEKVKALRGEIAPLKENVSHVNDLARQLTTL
                     GIQLSPYNLSTLEDLNTRWKLLQVAVEDRVRQLHEAHRDFGPASQHFLSTSVQGPWER
                     AISPNKVPYYINHETQTTCWDHPKMTELYQSLADLNNVRFSAYRTAMKLRRLQKALCL
                     DLLSLSAACDALDQHNLKQNDQPMDILQIINCLTTIYDRLEQEHNNLVNVPLCVDMCL
                     NWLLNVYDTGRTGRIRVLSFKTGIISLCKAHLEDKYRYLFKQVASSTGFCDQRRLGLL
                     LHDSIQIPRQLGEVASFGGSNIEPSVRSCFQFANNKPEIEAALFLDWMRLEPQSMVWL
                     PVLHRVAAAETAKHQAKCNICKECPIIGFRYRSLKHFNYDICQSCFFSGRVAKGHKMH
                     YPMVEYCTPTTSGEDVRDFAKVLKNKFRTKRYFAKHPRMGYLPVQTVLEGDNMETPVT
                     LINFWPVDSAPASSPQLSHDDTHSRIEHYASRLAEMENSNGSYLNDSISPNESIDDEH
                     LLIQHYCQSLNQDSPLSQPRSPAQILISLESEERGELERILADLEEENRNLQAEYDRL
                     KQQHEHKGLSPLPSPPEMMPTSPQSPRDAELIAEAKLLRQHKGRLEARMQILEDHNKQ
                     LESQLHRLRQLLEQPQAEAKVNGTTVSSPSTSLQRSDSSQPMLLRVVGSQTSDSMGEE
                     DLLSPPQDTSTGLEEVMEQLNNSFPSSRGRNTPGKPMREDTM"
     misc_feature    62..91
                     /note="Region: dystrophin Dp116 unique N-terminus"
     misc_feature    <92..994
                     /note="Region: central rod domain"
     misc_feature    <92..280
                     /note="Region: repeat region 22"
     misc_feature    281..667
                     /note="Region: repeat region 23"
     misc_feature    668..994
                     /note="Region: repeat region 24"
     misc_feature    914..1210
                     /note="Region: hinge region 4"
     misc_feature    1040..1150
                     /note="Region: WW-domain"
     misc_feature    1112..2098
                     /note="dystroglycan binding site"
     misc_feature    1172..1774
                     /note="Region: Cysteine-rich domain"
     misc_feature    1262..1345
                     /note="Region: EF-hand 1"
     misc_feature    1406..1492
                     /note="Region: EF-hand 2"
     misc_feature    1772..2929
                     /note="Region: Carboxy-terminal region"
     misc_feature    1793..1936
                     /note="Region: ZZ-domain"
     misc_feature    2204..2356
                     /note="alpha1-syntrophin binding site"
     misc_feature    2357..2479
                     /note="beta1-syntrophin binding site"
     misc_feature    2357..2479
                     /note="Region: beta1-syntrophin binding site"
     misc_feature    2546..2653
                     /note="Region: (Leu)6-heptad repeat"
     3'UTR           2933..5623
     polyA_signal    5601..5606
     polyA_site      5623
BASE COUNT     1696 a   1181 c   1171 g   1575 t
ORIGIN
        1 gggttttctc aggattgcta tgcaacagga tcagtgctgt agtgcccggt tcaagctgaa
       61 aatgttacac aggaagacat accatgtaaa ggacctccaa ggtgaaattg aagctcacac
      121 agatgtttat cacaacctgg atgaaaacag ccaaaaaatc ctgagatccc tggaaggttc
      181 cgatgatgca gtcctgttac aaagacgttt ggataacatg aacttcaagt ggagtgaact
      241 tcggaaaaag tctctcaaca ttaggtccca tttggaagcc agttctgacc agtggaagcg
      301 tctgcacctt tctctgcagg aacttctggt gtggctacag ctgaaagatg atgaattaag
      361 ccggcaggca cctattggag gcgactttcc agcagttcag aagcagaacg atgtacatag
      421 ggccttcaag agggaattga aaactaaaga acctgtaatc atgagtactc ttgagactgt
      481 acgaatattt ctgacagagc agcctttgga aggactagag aaactctacc aggagcccag
      541 agagctgcct cctgaggaga gagcccagaa tgtcactcgg cttctacgaa agcaggctga
      601 ggaggtcaat actgagtggg aaaaattgaa cctgcactcc gctgactggc agagaaaaat
      661 agatgagacc cttgaaagac tccaggaact tcaagaggcc acggatgagc tggacctcaa
      721 gctgcgccaa gctgaggtga tcaagggatc ctggcagccc gtgggcgatc tcctcattga
      781 ctctctccaa gatcacctcg agaaagtcaa ggcacttcga ggagaaattg cgcctctgaa
      841 agagaacgtg agccacgtca atgaccttgc tcgccagctt accactttgg gcattcagct
      901 ctcaccgtat aacctcagca ctctggaaga cctgaacacc agatggaagc ttctgcaggt
      961 ggccgtcgag gaccgagtca ggcagctgca tgaagcccac agggactttg gtccagcatc
     1021 tcagcacttt ctttccacgt ctgtccaggg tccctgggag agagccatct cgccaaacaa
     1081 agtgccctac tatatcaacc acgagactca aacaacttgc tgggaccatc ccaaaatgac
     1141 agagctctac cagtctttag ctgacctgaa taatgtcaga ttctcagctt ataggactgc
     1201 catgaaactc cgaagactgc agaaggccct ttgcttggat ctcttgagcc tgtcagctgc
     1261 atgtgatgcc ttggaccagc acaacctcaa gcaaaatgac cagcccatgg atatcctgca
     1321 gattattaat tgtttgacca ctatttatga ccgcctggag caagagcaca acaatttggt
     1381 caacgtccct ctctgcgtgg atatgtgtct gaactggctg ctgaatgttt atgatacggg
     1441 acgaacaggg aggatccgtg tcctgtcttt taaaactggc atcatttccc tgtgtaaagc
     1501 acatttggaa gacaagtaca gatacctttt caagcaagtg gcaagttcaa caggattttg
     1561 tgaccagcgc aggctgggcc tccttctgca tgattctatc caaattccaa gacagttggg
     1621 tgaagttgca tcctttgggg gcagtaacat tgagccaagt gtccggagct gcttccaatt
     1681 tgctaataat aagccagaga tcgaagcggc cctcttccta gactggatga gactggaacc
     1741 ccagtccatg gtgtggctgc ccgtcctgca cagagtggct gctgcagaaa ctgccaagca
     1801 tcaggccaaa tgtaacatct gcaaagagtg tccaatcatt ggattcaggt acaggagtct
     1861 aaagcacttt aattatgaca tctgccaaag ctgctttttt tctggtcgag ttgcaaaagg
     1921 ccataaaatg cactatccca tggtggaata ttgcactccg actacatcag gagaagatgt
     1981 tcgagacttt gccaaggtac taaaaaacaa atttcgaacc aaaaggtatt ttgcgaagca
     2041 tccccgaatg ggctacctgc cagtgcagac tgtcttagag ggggacaaca tggaaactcc
     2101 cgttactctg atcaacttct ggccagtaga ttctgcgcct gcctcgtccc ctcagctttc
     2161 acacgatgat actcattcac gcattgaaca ttatgctagc aggctagcag aaatggaaaa
     2221 cagcaatgga tcttatctaa atgatagcat ctctcctaat gagagcatag atgatgaaca
     2281 tttgttaatc cagcattact gccaaagttt gaaccaggac tcccccctga gccagcctcg
     2341 tagtcctgcc cagatcttga tttccttaga gagtgaggaa agaggggagc tagagagaat
     2401 cctagcagat cttgaggaag aaaacaggaa tctgcaagca gaatatgacc gtctaaagca
     2461 gcagcacgaa cataaaggcc tgtccccact gccgtcccct cctgaaatga tgcccacctc
     2521 tccccagagt ccccgggatg ctgagctcat tgctgaggcc aagctactgc gtcaacacaa
     2581 aggccgcctg gaagccagga tgcaaatcct ggaagaccac aataaacagc tggagtcaca
     2641 gttacacagg ctaaggcagc tgctggagca accccaggca gaggccaaag tgaatggcac
     2701 aacggtgtcc tctccttcta cctctctaca gaggtccgac agcagtcagc ctatgctgct
     2761 ccgagtggtt ggcagtcaaa cttcggactc catgggtgag gaagatcttc tcagtcctcc
     2821 ccaggacaca agcacagggt tagaggaggt gatggagcaa ctcaacaact ccttccctag
     2881 ttcaagagga agaaataccc ctggaaagcc aatgagagag gacacaatgt aggaagtctt
     2941 ttccacatgg cagatgattt gggcagagcg atggagtcct tagtatcagt catgacagat
     3001 gaagaaggag cagaataaat gttttacaac tcctgattcc cgcatggttt ttataatatt
     3061 catacaacaa agaggattag acagtaagag tttacaagaa ataaatctat atttttgtga
     3121 agggtagtgg tattatactg tagatttcag tagtttctaa gtctgttatt gttttgttaa
     3181 caatggcagg ttttacacgt ctatgcaatt gtacaaaaaa gttataagaa aactacatgt
     3241 aaaatcttga tagctaaata acttgccatt tctttatatg gaacgcattt tgggttgttt
     3301 aaaaatttat aacagttata aagaaagatt gtaaactaaa gtgtgcttta taaaaaaaag
     3361 ttgtttataa aaacccctaa aaacaaaaca aacacacaca cacacacata cacacacaca
     3421 cacaaaactt tgaggcagcg cattgttttg catccttttg gcgtgatatc catatgaaat
     3481 tcatggcttt ttcttttttt gcatattaaa gataagactt cctctaccac cacaccaaat
     3541 gactactaca cactgctcat ttgagaactg tcagctgagt ggggcaggct tgagttttca
     3601 tttcatatat ctatatgtct ataagtatat aaatactata gttatataga taaagagata
     3661 cgaatttcta tagactgact ttttccattt tttaaatgtt catgtcacat cctaatagaa
     3721 agaaattact tctagtcagt catccaggct tacctgcttg gtctagaatg gatttttccc
     3781 ggagccggaa gccaggagga aactacacca cactaaaaca ttgtctacag ctccagatgt
     3841 ttctcatttt aaacaacttt ccactgacaa cgaaagtaaa gtaaagtatt ggattttttt
     3901 aaagggaaca tgtgaatgaa tacacaggac ttattatatc agagtgagta atcggttggt
     3961 tggttgattg attgattgat tgatacattc agcttcctgc tgctagcaat gccacgattt
     4021 agatttaatg atgcttcagt ggaaatcaat cagaaggtat tctgaccttg tgaacatcag
     4081 aaggtatttt ttaactccca agcagtagca ggacgatgat agggctggag ggctatggat
     4141 tcccagccca tccctgtgaa ggagtaggcc actctttaag tgaaggattg gatgattgtt
     4201 cataatacat aaagttctct gtaattacaa ctaaattatt atgccctctt ctcacagtca
     4261 aaaggaactg ggtggtttgg tttttgttgc ttttttagat ttattgtccc atgtgggatg
     4321 agtttttaaa tgccacaaga cataatttaa aataaataaa ctttgggaaa aggtgtaaga
     4381 cagtagcccc atcacatttg tgatactgac aggtatcaac ccagaagccc atgaactgtg
     4441 tttccatcct ttgcatttct ctgcgagtag ttccacacag gtttgtaagt aagtaagaaa
     4501 gaaggcaaat tgattcaaat gttacaaaaa aacccttctt ggtggattag acaggttaaa
     4561 tatataaaca aacaaacaaa aattgctcaa aaaagaggag aaaagctcaa gaggaaaagc
     4621 taaggactgg taggaaaaag ctttactctt tcatgccatt ttatttcttt ttgattttta
     4681 aatcattcat tcaatagata ccaccgtgtg acctataatt ttgcaaatct gttacctctg
     4741 acatcaagtg taattagctt ttggagagtg ggctgacatc aagtgtaatt agcttttgga
     4801 gagtgggttt tgtccattat taataattaa ttaattaaca tcaaacacgg cttctcatgc
     4861 tatttctacc tcactttggt tttggggtgt tcctgataat tgtgcacacc tgagttcaca
     4921 gcttcaccac ttgtccattg cgttattttc tttttccttt ataattcttt ctttttcctt
     4981 cataattttc aaaagaaaac ccaaagctct aaggtaacaa attaccaaat tacatgaaga
     5041 tttggttttt gtcttgcatt tttttccttt atgtgacgct ggaccttttc tttacccaag
     5101 gatttttaaa actcagattt aaaacaaggg gttactttac atcctactaa gaagtttaag
     5161 taagtaagtt tcattctaaa atcagaggta aatagagtgc ataaataatt ttgttttaat
     5221 ctttttgttt ttcttttaga cacattagct ctggagtgag tctgtcataa tatttgaaca
     5281 aaaattgaga gctttattgc tgcattttaa gcataattaa tttggacatt atttcgtgtt
     5341 gtgttcttta taaccaccga gtattaaact gtaaatcata atgtaactga agcataaaca
     5401 tcacatggca tgttttgtca ttgttttcag gtactgagtt cttacttgag tatcataata
     5461 tattgtgttt taacaccaac actgtaacat ttacgaatta tttttttaaa cttcagtttt
     5521 actgcatttt cacaacatat cagacttcac caaatatatg ccttactatt gtattatagt
     5581 actgctttac tgtgtatctc aataaagcac gcagttatgt tac


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